TY - JOUR
T1 - Nomenclature of genetic movement disorders: Recommendations of the international Parkinson and movement disorder society task force
AU - Marras, Connie
AU - Lang, Anthony
AU - van de Warrenburg, Bart P.
AU - Sue, Carolyn M.
AU - Tabrizi, Sarah J.
AU - Bertram, Lars
AU - Mercimek-Mahmutoglu, Saadet
AU - Ebrahimi-Fakhari, Darius
AU - Warner, Thomas T.
AU - Durr, Alexandra
AU - Assmann, Birgit
AU - Lohmann, Katja
AU - Kostic, Vladimir
AU - Klein, Christine
PY - 2016/4/1
Y1 - 2016/4/1
N2 - The system of assigning locus symbols to specify chromosomal regions that are associated with a familial disorder has a number of problems when used as a reference list of genetically determined disorders,including (I) erroneously assigned loci, (II) duplicated loci, (III) missing symbols or loci, (IV) unconfirmed loci and genes, (V) a combination of causative genes and risk factor genes in the same list, and (VI) discordance between phenotype and list assignment. In this article, we report on the recommendations of the International Parkinson and Movement Disorder Society Task Force for Nomenclature of Genetic Movement Disorders and present a system for naming genetically determined movement disorders that addresses these problems. We demonstrate how the system would be applied to currently known genetically determined parkinsonism, dystonia, dominantly inherited ataxia, spastic paraparesis, chorea, paroxysmal movement disorders, neurodegeneration with brain iron accumulation, and primary familial brain calcifications. This system provides a resource for clinicians and researchers that, unlike the previous system, can be considered an accurate and criterion-based list of confirmed genetically determined movement disorders at the time it was last updated.
AB - The system of assigning locus symbols to specify chromosomal regions that are associated with a familial disorder has a number of problems when used as a reference list of genetically determined disorders,including (I) erroneously assigned loci, (II) duplicated loci, (III) missing symbols or loci, (IV) unconfirmed loci and genes, (V) a combination of causative genes and risk factor genes in the same list, and (VI) discordance between phenotype and list assignment. In this article, we report on the recommendations of the International Parkinson and Movement Disorder Society Task Force for Nomenclature of Genetic Movement Disorders and present a system for naming genetically determined movement disorders that addresses these problems. We demonstrate how the system would be applied to currently known genetically determined parkinsonism, dystonia, dominantly inherited ataxia, spastic paraparesis, chorea, paroxysmal movement disorders, neurodegeneration with brain iron accumulation, and primary familial brain calcifications. This system provides a resource for clinicians and researchers that, unlike the previous system, can be considered an accurate and criterion-based list of confirmed genetically determined movement disorders at the time it was last updated.
UR - http://www.scopus.com/inward/record.url?scp=84963550642&partnerID=8YFLogxK
U2 - 10.1002/mds.26527
DO - 10.1002/mds.26527
M3 - Journal articles
C2 - 27079681
AN - SCOPUS:84963550642
SN - 0885-3185
VL - 31
SP - 436
EP - 457
JO - Movement Disorders
JF - Movement Disorders
IS - 4
ER -