Pemphigus herpetiformis: From first description until now

Michael Kasperkiewicz*, Cezary Kowalewski, Stefania Jabłońska

*Korrespondierende/r Autor/-in für diese Arbeit
19 Zitate (Scopus)

Abstract

Pemphigus herpetiformis is one of the less common forms of pemphigus, first introduced by Jabłońska and colleagues in 1975. This autoimmune bullous disease combines the clinical features of dermatitis herpetiformis and the immunologic characteristics of pemphigus. The target autoantigen is usually desmoglein 1 (or less frequently desmoglein 3), although recently it has become increasingly obvious that patients with pemphigus herpetiformis also demonstrate autoantibodies against desmocollin. Here, we summarize reported cases of pemphigus herpetiformis and describe current knowledge considering epidemiology, clinical manifestations, histologic findings, immunopathology, pathophysiologic concepts, associated diseases, and treatment of this rare disorder.
OriginalspracheEnglisch
ZeitschriftJournal of the American Academy of Dermatology
Jahrgang70
Ausgabenummer4
Seiten (von - bis)780-787
Seitenumfang8
ISSN0190-9622
DOIs
PublikationsstatusVeröffentlicht - 01.01.2014

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